【摘要】 本文报道1例T1DM伴肝脏肿大患者，转氨酶升高，经肝脏穿刺诊断为糖原性肝病，经严格控制血糖5个月后复查转氨酶降至正常。

　　【关键词】 糖尿病，1型;糖原性肝病

　　【Summary】 The patient in the report is a case of hepatomegaly and elevated liver enzymes with T1DM, who was diagnosed as glycogenic hepatopathy by liver biopsy. The liver enzymes could be revert to normal by 5 months of strict glycemic control.

　　【Key words】 Diabetes mellitus, type 1; Glycogenic hepatopathy